Ehlers-Danlos Syndrome (EDS) : A Common and often Disregarded Cause of Serious Gastrointestinal Complications in Children and Adults

Ehlers-Danlos is a hereditary disease of the whole connective tissue initially described by dermatologists (Tscherchnogobov Moscow 1892, Ehlers, Copenhagen, 1900, Danlos, Paris, 1908). They emphasized joint hyperlaxity and stretchiness skin which has long summed up clinical expression this entity. In recent decades, many other manifestations have been gradually identified, mainly rheumatologists (Grahame, London, 1960). Several them concern digestive tract, gastric reflux constipation. can be cause serious accidents: bronchial flooding or aspiration, intestinal obstruction, hernial constriction, eventration, rupture, peritonitis vesicular appendicular origin, hemorrhages. It important that gastroenterologists know how to link these their etiology in order adapt treatments, prevent iatrogenic accidents direct patients towards treatment disease. Nine signs, including manifestations, allow diagnosis significant grouping. The proof origin based on identification identical cases family,, even if they are paucisymptomatic. A person affected systematically transmits all his children. We verified our patients.